Idiopathic Pulmonary Fibrosis - MedPix® Medical Image Database and Teaching Files

38.107.191.114

Disease Topic 1225
(Reviewed and Approved) :: Link to this Topic

Click Here for MedPix®-2

» » - - - - « «

Contributor: William J. Quinn - Tripler Army Medical Center

Scroll to Bottom to Display Images (if available)

Idiopathic Pulmonary Fibrosis
Factoid 1225 - Created: 2001-02-21 16:11:44-05 - Modified: 2001-02-26 11:52:21-05

ACR Codes: 68.792
Progressive inflammation, fibrosis, and destruction of lung (end-stage lung) of unknown cause. Synonyms: usual interstitial pneumonia (UIP, pathology term), cryptogenic fibrosing alveolitis (British term). Hamman-Rich syndrome is an acute, rapidly fatal form of IPF, and IPF has been termed "chronic Hamman-Rich syndrome." Prognosis: mean survival 4 years (range 0.4 to 20 years). Lung biopsy is necessary for diagnosis. Treatment: steroids, cytotoxic agents.
Clinical Findings:
-clubbing
-nonproductive cough
-dyspnea
-weight loss
Radiographic Features:
Distribution:
-primarily lower lung zones and peripheral subpleural involvement.
HRCT pattern:
-early: ground glass attenuation
-later: reticular pattern in lower lobes
-end-stage: honeycombing
-traction bronchiectasis indicates fibrosis

Reference(s):
Weissleder, et al. "Primer of Diagnostic Imaging", pp32-33, Mosby, 1997.

- || -

Location: Chest, Pulmonary (ex. Heart)	Sublocation: Pulmonary (lung)	Category: Idiopathic or Unknown
- Find Related Topics: Click on the Location, Sublocation, or Category Links Above

Send this Search to ...

- CHORUS - - Google™

Prepared by: William J. Quinn
Affiliation: Tripler Army Medical Center - || -
Approved by: David S. Feigin, M.D.
Affiliation: Johns Hopkins Hospitals - || -

Use this for Comments and Suggestions

MedPix® is sponsored by the Department of Radiology and Radiological Sciences, USUHS, Bethesda, MD
We do not accept paid advertisements.

We comply with the HONcode standard
for trustworthy health information:
verify here.

Text and Images may be Copyrighted © 1999 - 2009 by the Original Content Contributors.
Copyrighted materials are reproduced here with their Permission.
MedPix® is a Registered Trademark of USUHS :: The MedPix® Database Engine is Patented - USPTO No. 7,080,098
Portions of MedPix® are Copyright © 1999 - 2009 by J.G. Smirniotopoulos, M.D. & H. Irvine, M.D.
The MedPix® Classification Schema Copyright © 1999 - 2009 by J.G.Smirniotopoulos,M.D.

MedPix® has displayed more than 266,930,731 pages since 3 September 2000.

Database Successfully Disconnected