Tx and Followup:
Recommend 3 month follow up to document stability vs tissue biopsy.
Incidence: .15-2.8% of autopsies
Etiology: failure of involution of embryonic bile ducts
Associations: polycystic liver disease
Bile duct hamartoma, aka von Meyenburg complex, is a benign tumor composed of disorganized bile ducts and ductules and fibrocollagenous stroma. Although bile duct hamartoma is benign, there have been reports of an association of cholangiocarcinoma with multiple bile duct hamartomas.
Bile duct hamartoma has a nonspecific imaging appearance and can simulate metastases or microabscesses. Therefore, histologic diagnosis is required.